Intraventricular Baclofen via neuronavegated Ommaya reservoir as Bridge Therapy in Refractory Status Dystonicus: A Case Report

Authors

DOI:

https://doi.org/10.46900/apn.v7i3.318

Keywords:

stauts dystonicus, intraventricular baclofen, ommaya

Abstract

Introduction:
Status dystonicus (SD) is a life-threatening neurologic emergency that requires prompt recognition and intervention. Intraventricular baclofen (IVB) has been shown to be an alternative therapy with promising results in refractory cases.

Case Presentation:

We present a 12-year-old male with Wilson's disease and acquired generalized dystonia who developed status dystonicus after a gastrostomy procedure. Due to refractory, his dystonic symptoms despite of optimized intensive medical management, including intravenous sedation and invasive ventilatory assistance, we implemented intraventricular baclofen therapy via a temporary Ommaya reservoir. This allowed for rapid stabilization and resolution of the SD, prior to attempting to a more definitive surgical solution.

Conclusion:
Temporary Ommaya-based IVB is a feasible and cost-effective bridge therapy for SD management. It provides rapid symptomatic control and may enable strategic planning of definitive interventions, when applicable

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Published

2025-09-13

How to Cite

1.
de Oliveira AJB, Moller PD da S, Bastos A de MM, Cardoso KPO, Rodrigues BS, de Sousa RG. Intraventricular Baclofen via neuronavegated Ommaya reservoir as Bridge Therapy in Refractory Status Dystonicus: A Case Report. Arch Pediatr Neurosurg [Internet]. 2025 Sep. 13 [cited 2025 Sep. 26];7(3):e3182025. Available from: https://www.archpedneurosurg.com.br/sbnped2019/article/view/318