Non-traumatic epidural posterior fossa hematomas in child with Sensenbrenner syndrome: a case report and literature review

Authors

  • Mariana Mazzuia Guimarães Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0003-2946-5058
  • Daniel Dante Cardeal 1Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0002-2819-5415
  • José Erasmo Dal Col Lucio Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0001-9982-8673
  • Felipe Hada Sanders Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0003-3091-6266
  • Gustavo Correa Lordelo Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0003-3067-6880
  • Manoel Jacobsen Teixeira Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0002-7974-6045
  • Hamilton Matushita Division of Pediatric Neurosurgery, Department of Neurosurgery, Hospital das Clínicas, School of Medicine, University of São Paulo, Brazil https://orcid.org/0000-0001-5678-798X

DOI:

https://doi.org/10.46900/apn.v3i2(May-August).76

Keywords:

Epidural hematoma, Coagulopathy, Bleeding diathesis, Sensenbrenner syndrome, Ciliopathy

Abstract

Background: Posterior fossa extradural hematomas are an uncommon condition with more than half of cases appearing in the pediatric population. Although the majority of cases are caused by substantial trauma, it may also be related to systemic diseases and bleeding disorders without the history of head trauma.

Case report: We present the case of a 6-year-old female affected by Sensenbrenner syndrome with a non-traumatic subacute posterior fossa epidural hematoma. The patient was surgically treated and medically discharged without further neurological alteration. This is the first report of spontaneous cerebral hematoma associated with this syndrome in the literature. A literature review of the main aspects of both topics was performed.

Conclusions: Although spontaneous posterior fossa epidural hematomas are rare, clinicians should be aware and highly suspicious of this differential diagnosis in certain situations such as coagulopathies and other specific systemic diseases, as fast recognition and assertive treatment are important for better outcomes.

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Published

2021-05-06

How to Cite

1.
Guimarães MM, Cardeal DD, Lucio JEDC, Sanders FH, Lordelo GC, Teixeira MJ, Matushita H. Non-traumatic epidural posterior fossa hematomas in child with Sensenbrenner syndrome: a case report and literature review. Arch Pediat Neurosurg [Internet]. 2021May6 [cited 2021Jun.15];3(2(May-August):e762021. Available from: https://www.archpedneurosurg.com.br/pkp/index.php/sbnped2019/article/view/76

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